Dowling-Degos disease: An association with hidradenitis suppurativa
نویسندگان
چکیده
Dowling-Degos disease is one of the genodermatoses presenting with acquired reticulate pigmentation flexures, black-dot papules, and pitted scars. Numerous associated conditions multiple variants have been reported in literature. Several gene mutations play a role pathogenesis giving rise to phenotypic expressions. Herein, we discuss case three generations family affected shed light on associations various expressions disease.
منابع مشابه
Dowling-Degos disease associated with hidradenitis suppurativa: a case report.
Dowling-Degos disease (DDD) or reticular pigmented anomaly of the flexures is a rare autosomal dominant genodermatosis with variable penetrance. It mainly affects young women and is characterized by acquired reticular hyperpigmentation of the large skin folds. We present a case of DDD associated with hidradenitis suppurativa (HS) in a 43-year-old Spanish woman. Physical examination revealed bro...
متن کاملHidradenitis suppurativa, Dowling-Degos and multiple epidermal cysts: a new follicular occlusion triad.
This case illustrates the rare association between hidradenitis suppurativa (HS) and Dowling-Degos disease (DDD). Furthermore the association of HS, DDD and multiple epidermal cysts has not to our knowledge been described before, but their coexistence in the same patient is likely to reflect the same follicular anomaly. It is possible that a single underlying defect of follicular proliferation ...
متن کاملDowling-Degos disease.
Dowling-Degos disease (DDD) is a rare autosomal dominant inherited pigmentary disorder of the flexures with a reticulate aspect and with presence of prominent comedone-like lesions and pitted scars. The diagnosis includes acanthosis nigricans as well as other reticulate pigmentary disorders classified into: dyschromatrosis symmetrica hereditaria (DSH), dyschromatosis universalis hereditaria (DU...
متن کاملGeneralised Dowling-Degos Disease: A Rare Variant with Hypopigmented Macules
Dowling Degos disease is characterised by hyperpigmented macules arranged in a reticulate pattern in the flexures. The rare hypopigmented variant shows characteristic acanthosis with antler like rete ridges but with pigment only at the tips of the rete ridges. We describe here a rare variant with coexistence of characteristic reticulate hyperpigmentation and hypopigmented macules, which has bee...
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ژورنال
عنوان ژورنال: Our Dermatology Online
سال: 2022
ISSN: ['2081-9390']
DOI: https://doi.org/10.7241/ourd.20224.21